Syndrome ya Goodpasture

Matendawa amatchedwa chifuwa chachikulu cha mpweya ndi nephritis, kupweteka kwa mitsempha kapena idiopathic hemosiderosis. Dzina lake lenileni ndi matenda a Goodpasture. Ichi ndi matenda omwe sapezeka kwambiri omwe amakhudza munthu mmodzi pa milioni. Komabe muyenera kudziwa za zizindikiro zake, zizindikiro ndi njira zothandizira.

Zomwe zimayambitsa ndi zizindikiro za Kuperewera kwa Syndrome

Imeneyi ndi matenda opatsirana omwe amadziwika ndi matenda ndi zilonda zam'mimba za m'mapapo a alveoli. Mwachidziŵikire, matendawa amayamba mwa anthu omwe ali ndi chitetezo champhamvu ndipo amadziwika ndi kutaya magazi. Matenda Odziwika Omwe Amadziwika Ambiri Ambiri ndi Odwala Ambiri - Achinyamata. Matendawa amasankha amuna a zaka za pakati pa 18 ndi 35.

Ntchito za sayansi ndi zokhudzana ndi matenda a Goodpasture zakhala zolembedwa zambiri, koma palibe wasayansi atha kudziŵa chomwe chimayambitsa matendawa. Zimadziwika bwino kuti matendawa amachokera ku mapangidwe a ma antibodies omwe amachititsa kuti thupi liziyenda bwino. Zonsezi monga zotsatira zimayambitsa kuwonongeka kwa khoma lamtundu.

Pali malingaliro akuti Matenda a Goodpasture angayambitsidwe ndi matenda a tizilombo kapena mabakiteriya (monga, mwachitsanzo, kachilombo ka chiwindi). Kuwonjezera apo, zifukwa zina zingakhalenso ndi zotsatira zotsutsana ndi chitetezo cha mthupi. Monga momwe adasonyezera, osuta fodya amavutika nthawi zambiri. Zoopsa ndi anthu omwe amagwira ntchito pamalo oopsa, komanso omwe amamwa mankhwala ena, amavumbula.

Tikamakangana pazifukwa zomwe zimayambitsa matendawa, sitiyenera kuiwala za chibadwa chathu, ngakhale kuti matenda a Goodpasture ndi olakwika. Ndipo akatswiri ena amakhulupirira kuti matendawa amayamba kutsogolo kwa hypothermia.

Zizindikiro zoyamba za matenda a Goodpasture zimakhala zofanana ndi ziwonetsero za chikhalidwe cha pulmonary pathologies. Chinthu chosiyanitsa chachikulu ndi chitukuko chofulumira kwambiri. Mosiyana ndi chizoloŵezi chozizira, Matenda a Goodpasture kuyambira pachiyambi kupita kumalo osanyalanyazidwa angapitirire mu masiku amodzi.

Mawonetseredwe aakulu a matendawa ndi awa:

Kuzindikira ndi chithandizo cha matenda a Goodpasture

Ngati simusamala matenda a Goodpasture, ndiye kuti matendawa amatha kufa. Pofuna kupeŵa chithandizo chamankhwala chokwanira komanso chovuta, ndizokayikira koyamba ndi zofunika kuti mukafunse katswiri. Dziwani matendawa angakhale chifukwa cha kufufuza kwakukulu.

M'magazi a wodwalayo, phunzirolo lidzatha kudziwa kukhalapo kwa ma antibodies enieni. Kuwonjezera pamenepo, kukayikira kungachititse kuchepa kwa hemoglobini ndi kuchuluka kwa maselo ofiira a magazi. Mu kuyesa kwa magazi kwa matenda a Goodpasture amasonyeza kuchuluka kwa mapuloteni. Pa malo a roentgenogram malo otupa amawonekeratu.

Kuchiza kwa matenda a Goodpasture ngakhale m'mayambiriro oyambirira ayenera kukhala ovuta. Kawirikawiri mankhwalawa amaphatikizapo mankhwala osokoneza bongo komanso istiostatics. Odwala ena amafunika kusonyeza chithandizo chamankhwala m'malo mwake - kuika magazi a plasma ndi erythrocyte misa. Ngati matendawa amachititsa kuti thupi likhale lochepa, dialysis, ndipo nthawi zina ngakhale kuika, zingakhale zofunikira.