Cystic fibrosis ya mapapo

Pakati pa matenda omwe amayamba chifukwa cha jini, muthambo wam'mapapu uli pamwamba pa mndandanda. Matendawa akuphatikizidwa ndi kuphwanya chinsinsi cha zobisika zomwe zimayikidwa ndi ziwalo za thupi, zomwe zimapangitsa kugonjetsedwa kwa dongosolo la kupuma komanso m'mimba.

Matenda a mtundu wa cystic fibrosis

Nthendayi yotereyi imatchedwanso cystic fibrosis. Amadziwika ndi mitsempha yapamwamba komanso yowoneka bwino kwambiri ya ntchentche, yomwe imagwiritsa ntchito ziwalo zobowola. Chifukwa cha ndondomekoyi, kusungunuka kumatuluka, ndipo mabakiteriya omwe amachititsa kutupa akuchuluka.

Cystic fibrosis ya mapapo ali ndi chifukwa chimodzi - kuwonongeka kwa chromosome yachisanu ndi chiwiri (mkono wamtali). Malingana ndi ziwerengero, wonyamula matendawa ndi munthu aliyense wa makumi awiri padziko lapansi. Matendawa ndi 25%, ngati makolo onse ali ndi jini yoonongeka.

Pali mitundu itatu ya matenda awa:

Cystic fibrosis ya mapapo - zizindikiro

Zizindikiro zazikulu za matenda:

Mtundu wa cystic fibrosis umadziwonetsera m'zaka ziwiri zoyambirira za moyo, umadziwika kwambiri pakati ndi mwana wamng'ono wa bronchi.

Cystic Fibrosis - Kuzindikira ndi Kusanthula

Matendawa amapangidwa ndi zifukwa zinayi zofunika.

Choyamba, kupezeka kwa jini yowonongeka mwa makolo komanso zochitika m'banja zimayang'aniridwa. Zotsatira zabwino, komanso kupezeka kwa mapuloteni aakulu m'mapapu ndi bronchi, kupezeka kwa m'mimba matenda, kumapereka malo opangira thukuta. Zimaphatikizapo kudziƔa mlingo wa salt mumadzi otulutsidwa ndi pores. Pochita ndondomekoyi, malo ochepa pa mkono (pamwamba pa goli) amachizidwa ndi mankhwala apadera otchedwa pilocarpine. Ma electrode akuphatikizidwa ndi gawoli, zomwe zimapangitsa kuti thukuta limasulidwe, lomwe liri lokhalokha ndi pulasitiki kapena minofu yosungira, kutulutsa zotsatira za sauna. Pambuyo pa mphindi makumi anayi, madzi opangidwa ndi madziwa amawasanthula mchere. Ngati msinkhu wake umadutsa malire, maziko otsiriza amapangidwa.

Cystic fibrosis ya mankhwala

Chikhalidwe cha matendawa sichilola kuti kuchiritsidwa kwathunthu, mankhwalawa akukonzekera kuthetseratu zizindikiro ndipo amafuna njira yowonjezera. Chithandizo chili ndi zotsatirazi:

Wopambana komanso wogwira mtima panthawi yomwe njira yothandizira ndi yoperekera mapapo. Kuphatikiza apo, kufufuza kwachipatala kumachitika nthawi zonse kuti yothetse jini yowonongeka kwambiri pogwiritsa ntchito mavairasi opangidwa mwaluso.