Pakati pa matenda omwe amayamba chifukwa cha jini, muthambo wam'mapapu uli pamwamba pa mndandanda. Matendawa akuphatikizidwa ndi kuphwanya chinsinsi cha zobisika zomwe zimayikidwa ndi ziwalo za thupi, zomwe zimapangitsa kugonjetsedwa kwa dongosolo la kupuma komanso m'mimba.
Matenda a mtundu wa cystic fibrosis
Nthendayi yotereyi imatchedwanso cystic fibrosis. Amadziwika ndi mitsempha yapamwamba komanso yowoneka bwino kwambiri ya ntchentche, yomwe imagwiritsa ntchito ziwalo zobowola. Chifukwa cha ndondomekoyi, kusungunuka kumatuluka, ndipo mabakiteriya omwe amachititsa kutupa akuchuluka.
Cystic fibrosis ya mapapo ali ndi chifukwa chimodzi - kuwonongeka kwa chromosome yachisanu ndi chiwiri (mkono wamtali). Malingana ndi ziwerengero, wonyamula matendawa ndi munthu aliyense wa makumi awiri padziko lapansi. Matendawa ndi 25%, ngati makolo onse ali ndi jini yoonongeka.
Pali mitundu itatu ya matenda awa:
- m'mimba cystic fibrosis;
- pulmonary kapena kupuma cystic fibrosis;
- mitundu yosiyanasiyana (pulmonary cystic fibrosis).
Cystic fibrosis ya mapapo - zizindikiro
Zizindikiro zazikulu za matenda:
- msangamsanga wa mavenda okhwima;
- kuwonjezereka kambiri kwa chibayo, bronchitis, chibayo;
- kusokonezeka kwa matumbo;
- kutaya madzi;
- ululu, kusokonezeka mmimba;
- chilakolako chowonjezeka ndi kulemera kokwanira ndi chitukuko chakuthupi;
- zovuta zogonana;
- kupweteka ;
- kukulitsa kwa zala pa manja;
- matenda a chiwindi;
- shuga;
- sinusitis ;
- kupunduka kwa mafupa;
- Kuchuluka kwa matumbo (molunjika).
Mtundu wa cystic fibrosis umadziwonetsera m'zaka ziwiri zoyambirira za moyo, umadziwika kwambiri pakati ndi mwana wamng'ono wa bronchi.
Cystic Fibrosis - Kuzindikira ndi Kusanthula
Matendawa amapangidwa ndi zifukwa zinayi zofunika.
Choyamba, kupezeka kwa jini yowonongeka mwa makolo komanso zochitika m'banja zimayang'aniridwa. Zotsatira zabwino, komanso kupezeka kwa mapuloteni aakulu m'mapapu ndi bronchi, kupezeka kwa m'mimba matenda, kumapereka malo opangira thukuta. Zimaphatikizapo kudziƔa mlingo wa salt mumadzi otulutsidwa ndi pores. Pochita ndondomekoyi, malo ochepa pa mkono (pamwamba pa goli) amachizidwa ndi mankhwala apadera otchedwa pilocarpine. Ma electrode akuphatikizidwa ndi gawoli, zomwe zimapangitsa kuti thukuta limasulidwe, lomwe liri lokhalokha ndi pulasitiki kapena minofu yosungira, kutulutsa zotsatira za sauna. Pambuyo pa mphindi makumi anayi, madzi opangidwa ndi madziwa amawasanthula mchere. Ngati msinkhu wake umadutsa malire, maziko otsiriza amapangidwa.
Cystic fibrosis ya mankhwala
Chikhalidwe cha matendawa sichilola kuti kuchiritsidwa kwathunthu, mankhwalawa akukonzekera kuthetseratu zizindikiro ndipo amafuna njira yowonjezera. Chithandizo chili ndi zotsatirazi:
- maphunziro ambiri a antibiotics;
- mapulogalamu opangira phwando;
- kinesitherapy;
- Kuzizira kwa corticosteroid mahomoni ndi beta mimetics;
- kugwiritsa ntchito bronchodilator;
- kuchita masewera olimbitsa thupi;
- Kukonza chakudya ndi kuwonjezeka kwa malipiro a tsiku ndi tsiku ndi 10-15%;
- ngalande yamapapu yambiri;
- kachilombo-misala;
- phwando la mavitamini ndi microelements.
Wopambana komanso wogwira mtima panthawi yomwe njira yothandizira ndi yoperekera mapapo. Kuphatikiza apo, kufufuza kwachipatala kumachitika nthawi zonse kuti yothetse jini yowonongeka kwambiri pogwiritsa ntchito mavairasi opangidwa mwaluso.