Bullous pemphigoid

Nkhumba yamatenda kapena matenda a Lever ndi mtundu wambiri wa zilonda zamatenda ndi mapangidwe a mabelters. Kawirikawiri, matendawa amapezeka okalamba, a zaka 60 kapena kuposerapo, makamaka kawirikawiri ndi matendawa Levera amavutika ndi ana. Pachifukwa ichi, pemphigoid ndi yowonongeka, ndipo chithunzi chachipatala chimagwirizana kwambiri ndi zowopsya pemphigus, zomwe zimakhala zovuta kwambiri kuyeza ndikupeza mankhwala.

Zizindikiro za pemphgoid bullous

Kawirikawiri matendawa amakhudza khungu la thunthu ndi zowopsya, kawirikawiri pemphigoid imayika mapepala a mutu, nkhope ndi zikuluzikulu zazing'ono. Chizindikiro cha matenda a Lewra ndi kuphulika kwakukulu, kuti:

Zili ndi madzi omveka bwino, omwe amaletsedwa ndi matayala osokonekera. Si zachilendo khungu limene mabulters amaoneka ngati ali ndi thanzi labwino, koma nthawi zambiri limatulutsa ubweya wofiira, womwe ndi chizindikiro cha matendawa. Chithunzi cha kuchipatala chimaphatikizidwa ndi ziphuphu zamitundu yosiyanasiyana, zomwe zingawononge sarcoidosis molakwika.

Zizindikiro zolembedwazo ndizofunikira ndipo zimadziwonetsera m'masiku ochepa oyambirira, pambuyo pake ziphuphu ndi zotsegula zimatsegulidwa ndipo ziphuphu zoopsa zowonongeka zimapangidwira pamalo awo. Pankhani ya pemphigod yamphongo, zilonda sizinaphimbidwe ndi makoswe, koma epithelialized.

Nkofunikanso kuti m'thupi mwa munthu mmodzi pa asanu aliwonse, chiphuphu chimakhudza makamaka mlomo mucosa ndipo kenako nkuwoneka pakhungu.

Kuchiza kwa bullous pemphigoid

Chidziwitso cha chithandizo cha bullous pemphigoid kapena matenda a Lever ndi chakuti ayenera kukhala ovuta komanso munthu aliyense. Madokotala amasankha dongosolo la mankhwala pogwiritsa ntchito mfundo zotsatirazi:

Koma mulimonsemo, njira zazikulu zothandizira matenda a Lever ndi mankhwala omwe ali ndi glucocorticosteroids. Kumayambiriro kwa chithandizo, odwala amapereka 60-80 mg wa mankhwala mu maola 24. Pambuyo pake, dokotala, poganizira deta ili pamwambapa, amasintha mlingo.

Komanso pofuna kugwiritsa ntchito pemphigoid, ma immunosuppressants ndi cytostatics amagwiritsidwa ntchito. Mankhwalawa amaletsa chitetezo, komanso amachotsa chotupacho. Malingana ndi kuopsa kwa zizindikiro ndi msinkhu wa chitukuko chawo, mavitamini oterewa amauzidwa, kukonzekera kupangidwa kuchokera ku zosakaniza za michere ndi zinyama zamtundu zomwe zimakhudza njira za kutupa, njira zobwezeretsera ndi mayankho a chitetezo cha mthupi. Motero, vuto la wodwalayo limasintha kwambiri.