Galaulomatosis ya Wegener ndi matenda omwe amachititsa kuti matenda aakulu ndi ofulumira apite patsogolo. Vasculitis yowonongeka ndi granulomatosis ya Wegener ndizovuta kwambiri, chifukwa ma antibodies (antineutrophil cytoplasmic) amapangidwa mu granulomatosis, yomwe imakhala ndi mavoti a bungwe la ANCA.
Zifukwa za granulomatosis ya Wegener
Galaulomatosis ya Wegener imatanthawuzira kuimirira, kotero pakhoza kukhala ndi chibadwa. Ndipotu, granulomatosis ndiyomwe imateteza thupi lake. Choncho, zizindikiro za matendawa ndi antigen - HLA 〖B〗 _7, B_8,〗 DR〗 _2, 〖DQ〗 _w7.
Udindo wa tizilombo toyambitsa matenda umasewedwanso ndi tizilombo toyambitsa matenda omwe amachititsa kuti tizilombo toyambitsa matenda tizilombo toyambitsa matenda tizilombo toyambitsa matenda tizilombo toyambitsa matenda.
Galaulomatosis ya Wegener - zizindikiro
Zizindikiro za granulomatosis kawirikawiri zimachitika ali ndi zaka 40, pomwe nthendayi sizilibe kanthu.
Granulomatosis - kutukuta kwa makoma a zing'onozing'ono ndi zowonongeka: zotupa, ma capillaries, mitsempha ndi arterioles. Mu njira yogonjetsedwa, mapewa apamwamba, impso, maso, mapapo ndi ziwalo zina zimakhudzidwa.
Zizindikiro ndi izi:
- - kulemera, kufooka, myalgia, arthralgia, malungo, nthawi zambiri, nyamakazi;
- dongosolo la manjenje - losavomerezeka la polyneuropathy;
- maso - ischemia a mitsempha ya optic, khungu, episcleritis ndi granuloma orbital ndi exophthalmos;
- khungu - msuzi ndi ziwalo zonyansa;
- impso - glomerulonephritis , yomwe ingatenge nthawi yopuma;
- mapapu - zotupa zimakula mwa odwala 75% mwa mawonekedwe a infiltrates, omwe amapanga zibowo panthawi yovunda; ndi izi zikhoza kuwonedwa pleurisy, chifuwa.
- Mapepala a kupuma - amakhudzidwa ndi 90% mwa odwala monga rhinitis ndi chitetezo cha purulent-haemorrhagic ndi zilonda; Kuphulika kwa nsalu yamphongo kumabweretsa kusokonekera; Komanso, zilondazi zimakhudza zithunzithunzi, makutu, trachea, sinthana za paranasal, zomwe zimachitika mwachisawawa.
Granulomatosis ya Wegener ili ndi mitundu iwiri:
- malowa - amakhudza makamaka tsamba lopumako;
- Zachilengedwe - ndi ziwalo zambiri zimakhudzidwa, ndipo izi zimaphatikizapo kutentha thupi, zowawa, kuphwanya ndi mtima wosalimba.
Kuzindikira kwa granulomatosis ya Wegener
Izi zimapangidwa ndi rheumatologist kuchokera pa deta zingapo:
- kuyesa magazi - biochemical ndi ambiri, omwe sangathe kutsimikizira granulomatosis, koma kuthandizira kuthetsa matenda ena;
- Kusinkhasinkha kwa mkodzo - kumatha kutsimikizira kapena kusasamala kuwonongeka kwa impso (mawonekedwe a matendawa atsimikiziridwa);
- X-ray ya sinthana ya paranasal ndi thorax (computed tomography imapereka chidziwitso chochuluka kuposa chomwe chinapezedwa ndi X-ray);
- chiopsezo - njira yokhayo yomwe imatsimikizira momveka bwino kapena kukana kukhalapo kwa granulomatosis; Madokotala amachotsa minofu kapena mphuno, ndipo nthawi zina, impso ndi mapapo.
Kuchiza kwa granulomatosis ya Wegener
Chithandizo cha matendawa chikuchitika, makamaka, pogwiritsa ntchito corticosteroids ndi cytostatics, zomwe zimachepetsa ntchitoyo
Pakuwonongeka kwakukulu kwa impso, nthawi zina, wodwalayo akusowa chophimba.
Galaulomatosis ya Wegener - zizindikiro
Ngati chithandizo sichinayambidwe panthaŵi yake, ndiye kuti malingaliro oipawo adzakwaniritsidwa mkati mwa miyezi 6-12, ndipo chiwerengero cha moyo wosatha sichidutsa miyezi isanu.
Pankhani ya chithandizo, kukhululukira kumatha pafupifupi zaka 4, nthawi zina zaka 10. Chithandizo chonse pakadali pano cha chitukuko cha mankhwala sichingatheke.