Vuto la mwana wamadzimadzi ndi matenda omwe amakhudza makamaka khungu la khungu, komanso mitsempha ya m'magazi, ziwalo ndi impso. Ndilo gulu la ma immunocomplex osokoneza vasopathies a chilengedwe. Kuyamba kwa chitukukochi kumachitika pa msinkhu uliwonse, koma, monga lamulo, ana aang'ono (mpaka zaka zitatu) amadwala matendawa kawirikawiri.
Kaŵirikaŵiri, kupweteka kwa shuga kumapezeka kwa ana a zaka zapakati pa 4 mpaka 12.
Pali mitundu yosiyanasiyana ya mavenda othamanga magazi, osiyana ndi maonekedwe awo komanso chikhalidwe chawo. Choncho, matendawa amagawidwa m'magulu awiri: cholowa cha Hippel-Landau, Ehlers-Danlo, Matenda a Kazabaha-Merrita, Louis-Bar, ndi zina zotero) ndipo anapeza (mankhwala osokoneza bongo ndi chifuwa chosiyanasiyana, vasopathy, ndi zina zotero).
Vasculitis hemorrhagic: zimayambitsa
Matendawa amachititsidwa ndi kuwonongeka kwa makoma a capillary komanso kuwonjezeka kwa zowonongeka kwa zombo zonse, kuphatikizapo kuyambitsa njira yowonjezeramo komanso kuwonjezeka kwa chiwerengero cha ma chitetezo cha mthupi.
Kawirikawiri, chitukukochi chimayambira nthawi yayitali pambuyo pa matenda opatsirana (ARVI, matumbo, chifuwa chofiira, etc.). Nthaŵi zina chitukuko cha vasculitis chimayamba ndi kusagwirizana kwa mankhwala osokoneza bongo (kapena mitundu ina yowonongeka), hypothermia, katemera, zoopsa.
Zizindikiro za matenda opatsirana m'mimba mwa ana
Nthawi zambiri, chizindikiro choyamba cha matendawa ndi mawonekedwe a khungu kakang'ono ka mtundu wofiira. Mphuno ya misampha: zikopa za miyendo, mabowo, malo ozungulira. Kawirikawiri amawoneka pamphuno pamaso, palmu ndi mapazi, thunthu. Pambuyo pa kuthamanga, mdima wamdima umakhala m'malo mwake, umene umayamba kuchepa nthawi zambiri.
Chizindikiro chodziwika kwambiri ndicho kuwonongeka kwapadera. Zimapezeka kuyambira sabata yoyamba ya matenda. Chikhalidwe ndi nthawi ya ululu zingakhale zosiyana kwambiri, makamaka ziwalo zazikulu, makamaka mchiuno ndi mawondo, zimakhudzidwa. Pachifukwa ichi, ziwalozi zimapwetekedwa, koma palibe kuwonongeka kwabwino kwa thupi komanso kusokonezeka kwa thupi.
Chizindikiro chachitatu chofala kwambiri ndi kupweteka m'mimba. Zikhoza kusonyeza khungu ndi ziwalo kapena kuzigonjetsa. Kukumana ndi ululu kungabwereze mobwerezabwereza tsiku lonse, popanda kumveka bwino. Kawirikawiri, kunyowa, kusanza, ndi malungo zimayambanso. Nthawi zambiri, kupweteka kwa m'mimba kapena m'mimba kumatheka.
Nthaŵi zina ndi hemorrhagic vasculitis, chiwindi kapena ziwalo zina (mapapo, mtima, ziwiya za ubongo) zimakhudzidwa. Kulemera kwa zilonda kungakhale kosiyana - kuyambira pazing'ono, mpaka zovuta komanso zovuta.
Hemorrhagic vasculitis kwa ana: mankhwala
Chikhalidwe ndi njira za mankhwala zimasiyanasiyana malinga ndi chikhalidwe ndi mtundu wa matenda (vuto loyambalo, kubwereza kwa matenda kapena nthawi ya kukhululukidwa), pa mawonetseredwe a chipatala ndi kuuma, komanso pa nthawi yomwe ali ndi matendawa. Koma nkutheka kuti mutha kusankha mwapadera kwambiri, omwe amachitirako mankhwala.
Pa mitundu yonse ya matenda, antigregregants amagwiritsidwa ntchito. Perekani kurantil (persanthin, dipyridamole) 4 pa tsiku pa mlingo wa 5-8 mg pa kilogalamu ya thupi, trental (agapurine, pentoxifylline) katatu pa tsiku kwa 5-10 mg / kg kulemera kwa thupi. Pa milandu yoopsa, mitundu yonse ya mankhwalawa imatha kuperekedwa chimodzimodzi. Kutha kwa mankhwalawo kungakhale kosiyana - kuyambira miyezi 2 mpaka 12, malinga ndi kuopsa kwa matendawa. Fomu yopanda malire imapereka maphunziro ochuluka mobwerezabwereza (miyezi ingapo kapena miyezi isanu ndi umodzi).
Anti-coagulants amagwiritsidwa ntchito pa mlingo wina aliyense, opanga mafayili a fibrinolysis, enterosorbents, glucocorticosteroids, membrane stabilizers, cytostatics, antihistamines. Mankhwala opatsirana ndi plasmapheresis amagwiritsidwanso ntchito. Kusankha mankhwala ndi njira zothandizira ziyenera kuchitidwa ndi dokotala,
Kupewa kutentha kwa magazi
Ntchito yofunika kwambiri popewera matenda ndi kupewa, kupewa zoopsa za antchito opatsirana pogonana, kudzipatula ku zowonongeka. Odwala samapanga zitsanzo za mabakiteriya antigens (kuyesera kwa Burne, tuberculin, etc.). Kupewa kupweteka kwa magazi m'thupi n'kofunika kwambiri kwa hypoallergenic, kusala kudya, chakudya chopatsa thanzi komanso moyo wathanzi.