Cystic Fibrosis - Zizindikiro

Monga lamulo, n'zotheka kudziwa matenda a cystic fibrosis ali wamng'ono, chifukwa amadziwika ndi chizindikiro chodziwika bwino. Koma mu mawonekedwe a mtundu umodzi wofatsa kapena wochepa, matendawa amadziwonetsa bwino. Choncho ndikofunikira kudziwa, kuti tisiye kusiyanitsa ndi matenda ena ofanana mwachindunji cystic fibrosis - zizindikiro ndi zizindikiro zake zakunja.

Matenda a cystic fibrosis - ndi chiyani?

Matenda omwe ali mu funso ndi, m'malo mwake, matenda. Zimachokera ku kusintha kwa jini komwe kumapezeka kumbali yakutali ya chromosome yachisanu ndi chiwiri. Mpata wodwala ndizo ngati makolo onse akunyamula jini, ndipo ndi 25%. Ngakhale izi zili choncho, matenda a cystic fibrosis amakhudza anthu okwanira, popeza chromosome yomwe ili ndi kusintha kwapezeka kwa aliyense wakukhala 20 padziko lapansi.

Cystic Fibrosis mwa Anthu Achikulire - Zizindikiro

Monga taonera kale, matendawa amadziwonekera ali mwana, kawirikawiri mpaka zaka ziwiri, ndipo odwala 10 peresenti ali ndi zizindikiro zoyamba zikuwoneka paunyamata komanso akuluakulu.

Zizindikiro zazikulu za cystic fibrosis ndi izi:

Zizindikiro zolembedwa za cystic fibrosis zimagwirizana ndi kuti jini loonongeka sililola kuti thupi likhale ndi mapuloteni omwe amachititsa madzi omwe amadziwika kuti electrolyte metabolism m'maselo amkati. Izi zimabweretsa kuwonjezeka kwa kuchulukitsidwa kwa mchere komanso kutsekemera kwa madzi omwe amapangidwa ndi ma glands ambiri omwe amatuluka mkati. Mucus akutha, mabakiteriya amachulukira mmenemo, ndipo kusintha kosasinthika kumachitika mu ziwalo, makamaka m'mapapu.

Mtumbo wamatumbo wa cystic fibrosis umadziwika ndi kuphulika, kudula, kudzimbidwa ndi kusanza. Zizindikirozi ndizofunikira kuchiza mwakumwa mankhwala ndi michere, koma mawonetseredwe a matendawa akupitirira kuwonjezeka.

Cystic Fibrosis - Kudziwa

Choyamba, kukhalapo kwa zizindikiro zodziwika kwambiri za matendawa kumayang'aniridwa - mamasukidwe akayendedwe a chinsinsi cha ziwalo zamkati mkati, kuwonjezereka kwa matenda aakulu a kupuma. Pambuyo pa izi, nkofunika kukhazikitsa kukhalapo kwa jini losinthika kuchokera kwa makolo ndikuyang'ana milandu ya kufooka m'banja.

Kufufuza molondola kwambiri kwa cystic fibrosis ndi DNA. Chiyesochi ndi chovuta kwambiri, ndipo chikhoza kuchitidwa ngakhale panthawi ya mimba poyang'ana amniotic madzi. Chiwerengero cha zotsatira zabodza sichiposa 3% ndikukulolani kuti mumvetse mwamsanga popanda zina zowonjezera.

Kudziwa kuchuluka kwa mafuta acids ndi chymotrypsin mu chitseko cha wodwalayo ndi njira imodzi yodziwira matenda. Zizindikiro zosadziwika za chymotrypsin zimapangidwa payekha pa laboratory iliyonse. Kuchuluka kwa zidulo zomwe zimayambitsa kukayikira kwa cystic fibrosis ndizoposa 20-25 mmol pa tsiku.

Kujambula kwa cystic fibrosis ndi pilocarpine ndiko kufufuza kwa ma chlorides m'madzi omwe amadziwika ndi pores. Chiyesocho chiyenera kuyesedwa kasachepera katatu kuti chidziwike bwino.